Lymphangioleiomyomatosis

Lymphangioleiomyomatosis, or LAM, is a rare lung disease that manifests in adulthood and occurs almost exclusively in women. Patients suffer from cystic lung destruction and lyphatic abnormalities.

LAM can be a symptom of the tuberous sclerosis complex. Due to the heavy lung load, respiratory insufficiency can occur with LAM.

The cause of LAM, if it does not appear as a symptom of tuberous sclerosis, are mutations in the TSC1 and TSC2 genes.

Lymphangioleiomyomatosis, LAM for short, is a rare lung disease that manifests in adulthood and occurs almost exclusively in women. Patients suffer from cystic destruction of the lungs and lyphatic abnormalities.

LAM may be a symptom of the Tuberosal Sclerosis Complex. Due to the heavy lung load, respiratory insufficiency can occur with LAM.

Cause for the LAM, if it does not appear as a symptom of tuberous sclerosis, are mutations in the TSC1 and TSC2 genes.